Fast Facts for Patients: Thrombotic Thrombocytopenic Purpura : Prompt action saves lives

Thrombotic thrombocytopenic purpura (TTP) is a rare disorder of the blood coagulation system. In most cases, a lack of the ADAMTS13 enzyme leads to an accumulation of ultra-large von Willebrand factor molecules in the plasma which, in turn, initiate the formation of microscopic thromboses in small b...

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Hlavní autoři: Scully, Marie A., Cataland, S. R. (Autor), Thomas, Mari (Autor), Stubbs, Matthew (Autor)
Médium: Livre numérique
Jazyk:Anglais
Vydáno: Basel : S. Karger 2022.
Basel :
On-line přístup:https://www.karger.com/Book/Home/282612
Accès Université d'Orléans et IFPM
Poznámka: Karger Fast Facts
Autres localisations: Voir dans le Sudoc
Edition sous un autre format:• Fast Facts for Patients: Thrombotic Thrombocytopenic Purpura, 9783318070835
Popis
Shrnutí:Thrombotic thrombocytopenic purpura (TTP) is a rare disorder of the blood coagulation system. In most cases, a lack of the ADAMTS13 enzyme leads to an accumulation of ultra-large von Willebrand factor molecules in the plasma which, in turn, initiate the formation of microscopic thromboses in small blood vessels. TTP is a medical emergency. Timely diagnosis and urgent and effective management are vital - mortality in those untreated is in the region of 90%.The understanding of TTP pathogenesis has increased markedly in recent decades. It is now known that TTP is acquired (immunemediated) or congenital, and that the most common type - the acquired form - predominantly affects women in their 40s. It is also clear that the prompt delivery of plasma exchange saves lives. 'Fast Facts: Thrombotic Thrombocytopenic Purpura' sets out, in a clearand accessible format, the steps to suspecting, diagnosing and treating this potentially devastating disease
Popis jednotky:Karger Fast Facts
ISBN:9783318071221
Přístup:Accès libre pour tout établissement ou utilisateur ayant un compte sur la plateforme de l'éditeur